Hemophagocytic Lymphohistiocytosis: an update to diagnosis and management
نویسنده
چکیده
Hemophagocytic lymphohistiocytosis (HLH) is the uncontrolled reaction of the immune system against a triggering pathogen and inability of the immune system to elliminate this triggering factor, which ends up with hypercytokinemia and hemophagocytosis. Hemophagocytic lymphohistiocytosis is classified into two major groups as genetic (primary) and acquired (secondary). The condition has high mortality rates and specific tratment is required in most of the cases.
منابع مشابه
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متن کاملمعرفی یک مورد شیرخوار 50 روزه با بیماری لنفوهیستیوسیتوزیس هموفاگوسیتیک و علایم نارسایی کبدی
Expression of Hemophagocytic Lymphohistiocytosis with Hepatic Dysfunction in a 50 days Old Infant L. Borjian MD , H. Nazmieh MSc Received: 27/03/07 Sent for Revision: 13/06/07 Received Revised Manuscript: 08/07/07 Accepted: 26/07/07 Background and Objective: The Hemophagocytic Lymphohistiocytosis (HLH) is a rare disease with the pathologic hallmark of having aggressive proliferation o...
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تاریخ انتشار 2014